Specular microscopic findings of corneal deposits in patients with Bietti's crystalline corneal retinal dystrophy.
نویسندگان
چکیده
منابع مشابه
Bietti's tapetoretinal degeneration with marginal corneal dystrophy crystalline retinopathy.
In 1937 Bietti reported a tapetoretinal degeneration with associated corneal deposits at the limbus. The hallmark of the disease was the crystalline characteristics of the retinal spots as well as those at the corneal limbus. Bagolini and Ioli-Spade in 1968 presented a 30 year follow-up on Bietti's cases and presented six additional cases. The present report delas with this entity in Orientals,...
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Bietti's crystalline dystrophy (BCD) is a rare disease presenting with the appearance of intraretinal crystalline deposits and varying degrees of chorioretinal atrophy commencing at the posterior pole. Within time, intraretinal crystals gradually disappear and chorioretinal atrophy extends beyond the macula even resulting in complete chorioretinal atrophy. Concomitant corneal crystals can be no...
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ورودعنوان ژورنال:
- The British journal of ophthalmology
دوره 83 9 شماره
صفحات -
تاریخ انتشار 1999